metricas
covid
Buscar en
Revista Española de Medicina Nuclear e Imagen Molecular (English Edition)
Toda la web
Inicio Revista Española de Medicina Nuclear e Imagen Molecular (English Edition) IgG4-related disease
Journal Information
Vol. 40. Issue 2.
Pages 107-114 (March - April 2021)
Share
Share
Download PDF
More article options
Visits
5
Vol. 40. Issue 2.
Pages 107-114 (March - April 2021)
Special collaboration
IgG4-related disease
Enfermedad relacionada con IgG4
Visits
5
M. Simó-Perdigóa,
Corresponding author
marc.simo@quironsalud.es

Corresponding author.
, F. Martinez-Valleb
a Servicio de Medicina Nuclear, Hospital Vall d'Hebron, Barcelona, Spain
b Servicio de Medicina Interna, Unidad de Enfermedades Sistémicas, Hospital Universitario Vall d'Hebron, Barcelona, Spain
This item has received
Article information
Abstract
Full Text
Bibliography
Download PDF
Statistics
Figures (5)
Show moreShow less
Tables (1)
Table 1. Diseases within the spectrum of disease related to IgG4 and the organs affected (in parenthesis).
Abstract

IgG4-related disease (ER-IgG4) is a recognised systemic disease. It was described after patients diagnosed with autoimmune pancreatitis showed signs of extra-pancreatic disease. The clinical manifestation of these patients is subacute and is manifested by the appearance of pseudotumoral lesions, or inflammatory or fibrous tumours. Sometimes it can be serious as in the case of patients with cholangitis or large vessel vasculitis. Diagnostic criteria include, among others, serum IgG4 elevation and/or histological parameters. The 18F-FDG-PET/CT is useful in the initial diagnosis, biopsy guidance as well as in the assessment of response to therapy. It usually responds to steroid therapy.

Keywords:
IgG4-related disease
Autoimmune pancreatitis
18F-FDG-PET/CT
Index response
Plasmablasts
Resumen

La enfermedad relacionada con IgG4 (ER-IgG4) es una enfermedad sistémica reconocida. Se describió tras observarse que pacientes diagnosticados de pancreatitis autoinmune mostraban signos de enfermedad extra-pancreática. La clínica de estos pacientes es subaguda y se manifiesta por aparición de lesiones pseudotumorales, o tumores inflamatorios o fibrosos. En ocasiones puede ser grave como en la caso de pacientes con colangitis o vasculitis de gran vaso. Los criterios diagnósticos incluyen entre otros elevación sérica del valor de IgG4 y/o parámetros histológicos. La 18F-FDG-PET/TC es útil en el diagnóstico inicial, guía de biopsia así como en la valoración de respuesta a la terapia. Habitualmente responde al tratamiento con corticoides.

Palabras clave:
Enfermedad relacionada con IgG4
Pancreatitis autoimmune
18F-FDG-PET/TC
Responder index
Plasmablastos

Article

These are the options to access the full texts of the publication Revista Española de Medicina Nuclear e Imagen Molecular (English Edition)
Subscriber
Subscriber

If you already have your login data, please click here .

If you have forgotten your password you can you can recover it by clicking here and selecting the option “I have forgotten my password”
Subscribe
Subscribe to

Revista Española de Medicina Nuclear e Imagen Molecular (English Edition)

Purchase
Purchase article

Purchasing article the PDF version will be downloaded

Price 19.34 €

Purchase now
Contact
Phone for subscriptions and reporting of errors
From Monday to Friday from 9 a.m. to 6 p.m. (GMT + 1) except for the months of July and August which will be from 9 a.m. to 3 p.m.
Calls from Spain
932 415 960
Calls from outside Spain
+34 932 415 960
E-mail
Article options
es en pt

¿Es usted profesional sanitario apto para prescribir o dispensar medicamentos?

Are you a health professional able to prescribe or dispense drugs?

Você é um profissional de saúde habilitado a prescrever ou dispensar medicamentos