Megaesophagus secondary to Wilkie syndrome

We present the case of a 46-year-old woman diagnosed with megaoesophagus, with previous normal functional tests. Computed tomography showed megaoesophagus (Fig. 1A) secondary to a change in calibre in the third duodenal portion with an aortomesenteric distance of 6.2 mm (Fig. 1B) and an angle of 25° (Fig. 1C), characteristic of Wilkie’s syndrome. Her symptoms resolved after a duodenojejunostomy was performed, with adequate oral tolerance. Wilkie’s syndrome is an unusual cause, but should be included in the differential diagnosis of megaoesophagus.

Fig. 1