Journal of Plastic, Reconstructive & Aesthetic Surgery
Case ReportMonofocal maxillary fibrous dysplasia with orbital, nasal and oral obstruction
Section snippets
Case report
A 25-year-old male presented with a huge swelling (Figure 1) over his left maxillary region which was of insidious onset, painless and had gradually enlarged over a period of 15 years. As the swelling increased in size, it slowly began to obstruct his left nostril, causing difficulty in opening the left eyelids and the left side of the oral cavity resulting in an inability to chew food (Figure 2). On examination, there was a bony, hard swelling of 15 × 17 cm in size with peau d'orange appearance
Discussion
Fibrous dysplasia, also known as ossifying fibroma, is an uncommon condition of the bone which is characterised by excessive proliferation of bone-forming mesenchymal cells. The maxilla is the most commonly affected facial bone and the condition is usually seen in the first and second decade of life with a slight female preponderance, involving a single bone1 [monostotic] or multiple bones [polyostotic]. When monostotic fibrous dysplasia tends to impinge on the adjacent structures, it is known
Conflict of interest
There were no conflicts of interest either of ethical, academic or financial nature and there were no grants or sources of funding.
References (10)
- et al.
Fibrous dysplasia of bone: a condition affecting one, several or many bones, the graver cases of which may present abnormal pigmentation of skin, premature sexual development, hyperthyroidism or still other extra skeletal abnormalities
Arch Pathol
(1942) Fibrous dysplasia of the craniomaxillofacial region: current clinical perspectives
Br J Oral Maxillofac Surg
(1998)Osteitis fibrosa cystica: the case of a nine year old girl who also exhibits precocious puberty, multiple pigmentation of the skin and hyperthyroidism
Am J Dis Child
(1936)Fibrous dysplasia of single bones (monostotic fibrous dysplasia)
Mil Surg
(1946)- et al.
Increased proliferation of osteoblastic cells expressing the activating GS a mutation in monostotic and polyostotic fibrous dysplasia
Am J Pathol
(1997)
Cited by (8)
Management of fibrous dysplasia in the midface: Esthetic and functional considerations
2014, Revista Portuguesa de Estomatologia, Medicina Dentaria e Cirurgia MaxilofacialCitation Excerpt :Plastic surgery is often recommended when the jaws are involved.3 Conservative management has been the standard of care, which involves removing the diseased bone via an intraoral approach.1,4 In aberrant cases, orthognathic surgery is indicated to restore the occlusion and facial deformity.3
The role of multi-detector CT dacryocystography in the assessment of naso-lacrimal duct obstruction
2012, Egyptian Journal of Radiology and Nuclear MedicineCitation Excerpt :The added value of CT-DCG over CT was confirming the patency of the lacrimal duct system proximal to the obliterated level namely the canaliculi and the dilated lacrimal sac. Fibrous dysplasia involving the maxilla can result in nasal obstruction and orbital symptoms (27–30). NLDO secondary to an infective process presented on CT-DCG as dilated lacrimal sac with retained secretions and stranded surrounding fat planes.
Midfacial degloving approach for management of the maxillary fibrous dysplasia: a case report
2018, Maxillofacial Plastic and Reconstructive SurgeryGiant hemifacial fibrous dysplasia functional treatment and place of pamidronate
2017, Journal of Craniofacial SurgeryTreatment of fibrous dysplasia orbital deformities with digital imaging guidance
2015, Journal of Craniofacial SurgeryAn extensive hemimelic polyostotic fibrous dysplasia: A case report
2012, Rheumatology International