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Vol. 22. Issue 4.
Pages 192-194 (July - August 1986)
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Vol. 22. Issue 4.
Pages 192-194 (July - August 1986)
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Enfermedad pulmonar intersticial en la dermatomiositis
Interstitial pulmonary disease in dermatomyositis
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L. Dominguez juncal, A. Xaubet, C. Picado
Servei de Pneumologia. Hospital Clínic. Barcelona
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Se describen dos casos de afección pulmonar intersticial en el curso de una dermatomiositis. Las características clínicas, radiológicas, funcionales e histológicas de esta neumopatía intersticial son inespecíficas, siendo similares a las encontradas en pacientes con enfermedad intersticial pulmonar asociada a otras enfermedades del tejido conectivo o idiopáticas. Destaca el hecho de que, con frecuencia, la enfermedad pulmonar precede a la aparición de las manifestaciones extratorácicas.

Two case are described of interstitial pulmonary disease with dermatomyositis. The clinical, radiological, functional and histological characteristics of this type of interstitial pneumopathy are not specific and are similar to those seen in patients with interstitial pulmonary disease associated with other disorders of the connective tissues or idiopathic entities. It is note-worthy that the pulmonary disorder frequently precedes the appearance of extrathoracic manifestations.

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Copyright © 1986. Sociedad Española de Neumología y Cirugía Torácica
Archivos de Bronconeumología
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