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Vol. 31. Núm. 3.
Páginas 103-106 (Enero 2004)
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Vol. 31. Núm. 3.
Páginas 103-106 (Enero 2004)
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Telangiectasia hemorrágica hereditaria o síndrome de Rendu-Osler-Weber como causa de metrorragia posparto
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M.A. Barber, I. Eguiluz, W. Plasencia, C. Delgado, O. Ramírez
Servicio de Obstetricia y Ginecología. Hospital Universitario Materno-Infantil de Canarias. Las Palmas de Gran Canaria. España.
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Resumen

La telangiectasia hemorrágica hereditaria es un trastorno hereditario de los vasos sanguíneos que afecta a uno entre 5.000-8.000; se caracteriza por telangiectasias mucocutáneas y malformaciones arteriovenosas que pueden ocasionar sangrado excesivo y síndrome anémico. La telangiectasia hemorrágica hereditaria,conocida también como THH o síndrome de RenduOslerWeber,se hereda como un rasgo autosómico dominante. Describimos un caso clínico que cursó con metrorragia posparto importante,que requirió tratamiento médico enérgico. Realizamos una revisión bibliográfica enfocada en el manejo de dicha entidad durante el parto y el puerperio.

Abstract

Hereditary haemorrhagic telangiectasia (HHT) is a condition of the blood vessels which affects one in every 5-8000, and is characterized by mucocutaneous telangiectasia and arterio-venous malformations, causing abnormal bleeding and anaemia syndrome. HHT is also known as Rendu-Osler-Weber syndrome, and is inherited as an autosomal dominant trait. We describe a case of important postpartum bleeding, which required medical treatment. A bibliographic review focuses on HHT management during pregnancy and postpartum.

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Bibliografía
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Copyright © 2004. Elsevier España, S.L.. Todos los derechos reservados
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