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Case Report
Sneddon syndrome associated with antiphospholipid syndrome: Clinical descriptions and a literature review
Síndrome de Sneddon asociado a síndrome antifosfolipídico: descripciones clínicas y revisión de la literatura
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Cesar R. Carpio-Chanamea,b, Stalin Vilchez-Riveraa,b, Virgilio E. Failoc-Rojasa,b,
Corresponding author
virgiliofr@gmail.com

Corresponding author.
a Servicio de Medicina Interna, Hospital Regional Lambayeque, Lambayeque, Peru
b Facultad Medicina Humana, Universidad Nacional Pedro Ruiz Gallo, Lambayeque, Peru
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Received 09 December 2016. Accepted 08 February 2017
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Abstract

Sneddon syndrome is a rare non-inflammatory obliterative vasculopathy, characterized by the association of cardiovascular (arterial hypertension, intermittent claudication, and coronary artery disease) and neurological events (ischemic stroke, headache, dizziness and convulsions), and livedo reticularis/livedo racemosa. The case is presented of a woman admitted with an ischemic neurological disease, hypertension, vascular problems, and skin lesions. The skin biopsy was classified as surface perivascular lymphocytic dermatitis, suggestive of occlusive lesion.

Keywords:
Sneddon syndrome
Livedo reticularis
Antiphospholipid syndrome
Resumen

El síndrome de Sneddon es una rara vasculopatía no inflamatoria, obliterante, caracterizada por la asociación de eventos cardiovasculares (hipertensión arterial, claudicación intermitente y enfermedad coronaria), neurológicas (accidentes cerebrovasculares isquémicos, cefalea, vértigo y convulsiones) y livedo reticularis de tipo racemosa. Presentamos a una mujer que ingresa con un cuadro neurológico isquémico, hipertensión arterial, problemas vasculares y lesiones en piel. La biopsia de piel se catalogó como dermatitis perivascular superficial linfocitaria, sugestivo de lesión oclusiva.

Palabras clave:
Síndrome de Sneddon
Livedo reticularis
Síndrome antifosfolípido

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